Introduction: Congenital femoral deficiency (CFD) is a rare condition, with various classifications. Few have reported on the valgus derotation osteotomy for the correction of coxa vara deformity in CFD. We report our experience in coxa vara correction in cases of congenital femoral deficiency.
Patients and Methods: Six cases with congenital femoral deficiency with the bone abnormality presented in the form of femoral shortening with coxa vara without acetabular dysplasia, cases were classified according to Paley’s (only CFD type 1 were included). Cox avara correction was done using a locked proximal femoral plate with femoral shortening and soft tissue release. Average follow-up was 13 months. Evaluation of the outcome was done radiologically and clinically using the Children's hospital Oakland hip evaluation scale (CHOES)
Results: Radiographic union was achieved in all cases at 6 weeks follow-up as evident by bridging callus on at least 3 cortices. CHOES score was excellent in 2 cases and good in 4 cases. We had no significant complication in any of the cases at final follow-up.
Conclusion: Valgus derotation osteotomy with adequate shortening and soft tissue release for the correction of proximal femoral varus in CFD using locked is safe, reliable with minimal complications.